Catherine Wong

Sep 4, 2024 | scirp.org | Elaine Chau |Catherine Wong |Raymond Liang

1. IntroductionImmunoglobulin G4 (IgG4)-related disease (IgG4-RD) is a systemic immune-related condition that was first recognized in 2003 and is characterized by infiltration of IgG4-positive plasma cells and fibrosis in systemic organs and elevation of serum IgG4 levels. Approximately 1/5 of IgG4-RD patients have large vessel involvement in the form of aortitis or periaortitis [1] [2]. IgG4-related coronary arteritis cases are rare and limited to case reports and small case series [3]-[8].