Sara Patrizi

2 months ago | onlinelibrary.wiley.com | Emma Rullo |Sabina Barresi |Sabrina Rossi |Sara Patrizi

1 Introduction Congenital peribronchial myofibroblastic tumor (CPMT) is recognized by the Pediatric WHO classification, 5th edition, as an extremely rare myofibroblastic neoplasm of the lung, with less than 24 cases reported so far, all developing in utero or during infancy [1-21] (Table 1). CPMT is characterized by histologically bland myofibroblasts arranged in intersecting fascicles with a benign-appearing cartilage component.