Complex Diseases

Sep 18, 2024 | onlinelibrary.wiley.com | Maddalena Rossi |Complex Diseases |Enrico Fabris |Gianfranco Sinagra

Corresponding Author Gianfranco Sinagra Cardiothoracovascular Department, Center for Diagnosis and Treatment of Cardiomyopathies, Azienda Sanitaria Universitaria Giuliano-Isontina, University of Trieste, Trieste, Italy European Reference Network for Rare, Low-Prevalence, and Complex Diseases of the Heart (ERN GUARD-Heart) Corresponding author. Cardiothoracovascular Department, University of Trieste, Via Valdoni 7, 34129 Trieste, Italy.

Jan 9, 2024 | academic.oup.com | Johns Hopkins |De Marco |Complex Diseases

Arrhythmogenic right ventricular cardiomyopathy (ARVC) is an inherited cardiomyopathy characterized by progressive fibro-fatty replacement of the myocardium which predisposes patients to ventricular arrhythmias (VAs) and sudden cardiac death (SCD).1 Prevention of SCD through the placement of an implantable cardioverter-defibrillator (ICD) thus represents a mainstay of ARVC management.